Terrien, degeneration, cornea, thinning, astigmatism. We report a case of a 55yearold woman with systemic. The prevalence and aetiology of this disorder remain unknown. Unilateral superior pellucid marginal degeneration in a. Pellucid marginal degeneration genetic and rare diseases. Pellucid marginal degeneration pmd clinical presentation. If you have problems viewing pdf files, download the latest version of adobe reader.
Pellucid marginal degeneration pmd differential diagnoses. Pellucid marginal degeneration pmd is a noninflammatory, nonhereditary cause of corneal ectasia with bilateral, clear, inferior typically 4 oclock to 8 oclock, peripheral corneal thinning. Degeneracion marginal pelucida y ulcera corneal asociadas a. It typically presents with painless vision loss affecting both eyes. Rarely, it may cause acute vision loss with severe pain due to perforation of the cornea.
Although complementary tests can be very useful in the diagnosis, followup and management of this pathology, especially in atypical presentations. Current options in the management of pellucid marginal. Degeneracion marginal pelucida blog visual center madhu. Degeneracion marginal pelucida dmp epidemiologia causas. The academy uses cookies to analyze performance and provide relevant personalized content to users of our website. It is typically characterized by a clear, bilateral thinning in the inferior and peripheral region of the cornea, although some. Oct 30, 2017 pellucid marginal degeneration and bilateral corneal perforation. Pellucid marginal degeneration pmd, is a degenerative corneal condition, often confused with keratoconus. Unilateral pellucid marginal degeneration in an elderly patient. All structured data from the file and property namespaces is available under the creative commons cc0 license. Degeneracion marginal pelucida almeria andalucia qvision. Pellucid marginal corneal degeneration pmcd is an uncommon cause of inferior peripheral corneal ectasia, affecting patients between the ages of 20 and 40 years. Caracteristicamente aparece en cornea periferica inferior. Pdf pellucid marginal degeneration is characterized by a progressive stromal thinning of the inferior corneal segment, between 4 and 8 oclock, with a.
Terrien marginal corneal degeneration is a rare eye disease, generally bilateral and asymmetrical, which is characterized by marginal attenuation of the cornea. Corneal perforation associated with pellucid marginal degeneration and treatment with crescentic lamellar keratoplasty. Jessica rodriguez bonet, alexandre saintjean riquelme, carlos peralvarez conde, diana paola pinilla fuentes, manuel alexander castro diaz. Many patients will have some history of allergy, asthma, eczema andor hay. To present a case of bilateral atipic terriens marginal degeneration. Files are available under licenses specified on their description page. Pellucid marginal degeneration is characterised by non inflammatory and progressive peripheral corneal thinning inferiorly, often with high againsttherule astigmatism. May 01, 1987 mm rodrigues, da newsome, jh krachmer, a eifermanpellucid marginal corneal degeneration. Pellucid marginal degeneration pmd is a noninflammatory and progressive ectatic corneal disease characterized by a narrow band of corneal thinning 12 mm from the limbus commonly inferior. Afecta tanto a cornea superior como a inferior, con vascularizacion y depositos lipidicos. A degeneracao marginal pelucida dmp e uma ectasia corneana rara.
Degeneracion marginal pelucida ectasia corneal clinica rahhal. This rare entity has been postulated to be an abnormality. Apr 01, 2011 pellucid marginal corneal degeneration pmd is a rare ectatic disorder which typically affects the inferior peripheral cornea in a crescentic fashion. It is present a case of masculine patient that have 80 years old with terriens marginal degeneration, in the right eye the disease is in the marginal opacity similarly to gerontoxon without vascularization and in the left eye in marginal groove, localized in inferior sector in 2 eyes. Corneoescleral freehand lamellar keratoplasty in terriens marginal degeneration of the cornea.
Terriens marginal degeneration is a rare condition and patients are mainly clinical diagnosed. Caracterizase por afinamento periferico, sem sinais. Unilateral pellucid marginal degeneration in an elderly. Keratoconus and related noninflammatory corneal thinning disorders. Corneal topography of pellucid marginal degeneration.
830 1182 110 11 230 534 1356 494 20 615 1085 1094 599 710 315 408 976 1330 171 350 1211 265 1269 338 454 397 1231 844 860 755 229 994 257 431 957 741 215 162 1060